Presku: | AAP56116 |
Size: | 100 ug |
Weight: | 58kDa |
Gene: | 5096 |
Format: | Lyophilized powder |
Target: | PCCB is a subunit of the propionyl-CoA carboxylase (PCC) enzyme, which is involved in the catabolism of propionyl-CoA. PCC is a mitochondrial enzyme that probably acts as a dodecamer of six alpha subunits and six beta subunits. Defects in this gene are a cause of propionic acidemia type II (PA-2). |
Alternative names: | DKFZp451E113 |