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ECE-1 Antibody

ECE-1 Antibody

Cat no: 251559


Supplier: ABBIOTEC
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Endothelin-converting enzyme 1 (ECE-1) is an enzyme that hydrolyzes hydrolysis the 21-Trp-|-Val-22 bond in big endothelin, thus forming endothelin 1. Defects in ECE-1 are a cause of Hirschsprung disease, cardiac defects and autonomic dysfunction (HSCRCDAD). It is a form of Hirschsprung disease with skip-lesions defects, craniofacial abnormalities and other dysmorphic features, and autonomic dysfunction.
Catalogue number: 251559
Reactivities: Human, Mouse, Rabbit
Applications: Immunohistochemistry
Size: 0.1 mg
Accession: P42892
Antigen: KLH-conjugated synthetic peptide encompassing a sequence within the N-term region of human ECE-1.
Format: Each vial contains 0.1 mg IgG in 0.1 ml (1 mg/ml) of PBS pH7.4 with 0.09% sodium azide. Antibody was purified by immunogen affinity chromatography.
P type: Rabbit Polyclonal Antibody
Isotype: Rabbit Ig
Additional info: ECE1; Endothelin-converting enzyme 1; ECE-1